Endothelin receptor Antagonists
Ambrisentan
ARIES 1
6MWD improved TTCW not improved
Bosentan
BREATHE 1
6MWD improved TTCW improved
PDE 5 Inhibitors
Sildenafil
SUPER 1
6MWD improved TTCW not improved
Guanylate cyclase stimulators
Riociguat
PATENT
6MWD improved Haemodynamics improved
Prostacyclin analogues